Macrodystrophia Lipomatosa of the hand

Rai, Santosh and Chakraborti, Shrijeet (2013) Macrodystrophia Lipomatosa of the hand. International Journal of Medical and Applied Sciences, 2 (4). pp. 43-46. ISSN 2320‐3137

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Macrodystrophia Lipomatosa is an unusual form of localized gigantism. Lower limb is more frequently involved than upper limbs. Here we report a case of Macrodystrophia Lipomatosa of the hand. We describe the characteristic radiographic and MRI findings that distinguish the abnormality from other causes of localized gigantism. MR images confirmed excess fatty proliferation and fatty infiltration of the involved muscles. MR angiography did not show any significant vascular supply to the lesions. These findings were sufficed for giving a radiological diagnosis of Macrodystrophia Lipomatosa. After cosmetic surgery, histopathology of specimen showed massive increase in adipose tissue, interspersed in a fine mesh of fibrous tissue associated with fibrolipomatous hamartoma of a plantar nerve. Radiological findings can be used to confidently diagnose and differentiate this condition from other conditions causing localized gigantism. This differentiation is significant since the various conditions causing localized gigantism differ in their course, prognosis, complications and treatment.

Item Type: Article
Uncontrolled Keywords: gigantism, macrodystrophia lipomatosa, MR imaging.
Subjects: Medicine > KMC Mangalore > Pathology
Medicine > KMC Mangalore > Radio Diagnosis and Imaging
Depositing User: KMCMLR User
Date Deposited: 20 Nov 2013 05:28
Last Modified: 20 Nov 2013 05:28

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