A Case of Klippel Trenaunay Syndrome and Review of Literature

Selvaraju, K and Shenoy, MG and Bandari, S (2012) A Case of Klippel Trenaunay Syndrome and Review of Literature. WebmedCentral SURGERY, 3 (12). pp. 1-6.

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Abstract

Klippel-Trenaunay syndrome is a capillary-lymphatic-venous malformation 1. That is characterized by a triad of port-wine stain, varicose veins, and bony and soft tissue hypertrophy 2. High-flow high-shunt arteriovenous fistulae are characteristics of Parkes-Weber syndrome, a malformation that has significantly more hemodynamic complications. The cause of KTS remains obscure. Several theories exist like intrauterine injury to the sympathetic ganglia 3. deep vein abnormalities 4. mesodermal defect 5. mutated angiogenic factor gene 6. The management for the various components of this syndrome remains controversy. Here we present a 14 years old boy with KTS and discussed the management of often challenging components of this syndrome

Item Type: Article
Uncontrolled Keywords: Klippel-Trenaunay-Weber Syndrome; KTS; Angio-Osteohypertrophy; Nevus varicosus osteohypertrophicus syndrome; Hemangiectasia hypertrophicans; Nevus verucosus hypertrophicans
Subjects: Medicine > KMC Manipal > Surgery
Depositing User: KMC Manipal
Date Deposited: 09 Jan 2013 09:46
Last Modified: 09 Jan 2013 09:46
URI: http://eprints.manipal.edu/id/eprint/77909

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